HEART TRANSPLANTATION IN LEFT VENTRICULAR NON-COMPACTION: FIRST CASE IN PANAMA

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Published: 2019-12-01
DOI: https://doi.org/10.64738/rmcss.41.33
Keywords:
noncompaction of the left ventricular myocardium, heart failure, heart transplantation

Main Article Content

Miguel Ángel Valdés Camaño
Complejo Hospitalario Dr. Arnulfo Arias Madrid
Temístocles Díaz
Hospital Punta Pacífica 
Milantia Roy
Hospital Punta Pacífica 
José López
Complejo Hospitalario Dr. Arnulfo Arias Madrid 

Abstract


Left ventricular non-compaction or noncompaction of the left ventricular myocardium is a congenital cardiomyopathy that represents 0.01-0.17% of cardiomyopathies. It manifests clinically with the classical triad of heart failure, arrhythmias and thromboembolic events. Its prognosis is poor, with high morbidity and mortality, and medical management is directed to clinical manifestations. Cardiac transplantation is a therapeutic option for cases with advanced heart failure. We present a 19-year-old male patient with left ventricular non-compaction and advanced heart failure, who underwent heart transplantation.

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Article Details

Issue

Vol. 41 (2019)

Section

Caso clínico
Creative Commons License

This work is licensed under a Creative Commons Attribution-NonCommercial 4.0 International License.

Author Biographies

Miguel Ángel Valdés Camaño, Complejo Hospitalario Dr. Arnulfo Arias Madrid

Especialista en Medicina Interna y Médico Residente de Cardiología. Complejo Hospitalario Dr. Arnulfo Arias Madrid. 

Temístocles Díaz, Hospital Punta Pacífica 

Médico Especialista en Medicina Interna, Cardiología Clínica y Cardiología Intervencionista. Hospital Punta Pacífica 

Milantia Roy, Hospital Punta Pacífica 

Médico Especialista en Patología. Hospital Punta Pacífica 

José López, Complejo Hospitalario Dr. Arnulfo Arias Madrid 

Médico Especialista en Medicina Interna, Cardiología y Ecocardiografía. Complejo Hospitalario Dr. Arnulfo Arias Madrid 

How to Cite

1.
HEART TRANSPLANTATION IN LEFT VENTRICULAR NON-COMPACTION: FIRST CASE IN PANAMA. RMCSS [Internet]. 2019 Dec. 1 [cited 2025 Aug. 28];41:59-62. Available from: https://revistamedicacss.edu.pa/rmcss/article/view/33

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